Deficiency of plasminogen activator inhibitor 2 in plasma of patients with hereditary angioedema with normal C1 inhibitor levels.

Hereditary angioedema with normal levels of C1 inhibitor (HAE-N) is associated with mutations in Factor XII in 30% of subjects; However, the role of this mutation in the pathogenesis of angioedema is unclear.
We are looking for evidence
of abnormalities in the pathway of bradykinin bradykinin formation and degradation in the plasma of patients with HAE-N both with and without the mutation.


Bradykinin has been added to the plasma, and the degradation rate was measured using ELISA. autoactivation Plasma assessed using a chromogenic assay kallikrein formation. Plasminogen activator inhibitor (Pais) 1 and 2 were measured by ELISA method.


PAI-1 levels varied from 0.1 to 4.5 ng / mL (median, 2.4 ng / mL) in 23 control subjects, 0.0 to 2 ng / mL (mean, 0.54 ng / ml) in patients with HAE-N with factor XII mutations (12 samples), and 0.0 to 3.7 ng / mL (mean, 1.03 ng / mL) in patients with HAE-N without factor XII mutation (11 samples). PAI-2 levels vary 25-87 ng / mL (median, 53.8 ng / mL) in control subjects and 0-25 ng / mL (median, 4.3 ng / mL) in patients with HAE- N with or without the mutation Factor XII. Autoactivation at 1: 2 dilution is abnormally high in 8 of 17 patients with HAE-N (4 in each sub-category) and can be corrected with additional C1 inhibitor in 4 of them. bradykinin degradation is real abnormal in 1 out of 23 patients with HAE-N and normal in the remaining 22 patients.


bradykinin degradation is normal in all but one of 23 patients with HAE-N studied. Conversely, there are disorders characterized in PAI-2 levels in patients with HAE-N were not seen in patients with C1 inhibitor deficiency. PAI-1 levels vary, but the difference was not statistically significant visible. A link between excessive fibrinolysis and bradykinin generation suggested that estrogen dependent.

Deficiency of <em>plasminogen</em> <em>activator</em> <em>inhibitor</em> <em>2</em> in plasma of patients with hereditary angioedema with normal C1 <em>inhibitor</em> levels.
Deficiency of plasminogen activator inhibitor 2 in plasma of patients with hereditary angioedema with normal C1 inhibitor levels.

Copper (II) ions Increases Plasminogen Activator Inhibitor Type 1 Structural Dynamics in Key Regions Memerintah Stability.

Plasminogen activator inhibitor type 1 (PAI-1) regulates the fibrinolysis pathway by inhibiting the protease activity of plasminogen activators. PAI-1 works in concert with vitronectin (VN), an extracellular protein that aids in localization of active PAI-1 to the network. Peterson laboratory showed that Cu (II) and other transition metals modulate the stability of PAI-1, the effect of which depends on the presence or absence of somatomedin B (SMB) domain of VN show.

The studies presented here dissect the molecular changes underlying dynamics destabilizing effect of Cu (II) on PAI-1. We use exchange backbone amide hydrogen / deuterium monitored by mass spectrometry to assess the dynamics of PAI-1 in the presence and absence of Cu (II) ion with and without the SMB domain of VN. We show that Cu (II) results in improved dynamics in areas essential to the function and the overall stability of PAI-1, whereas the SMB domain elicits almost the opposite effect.

A mutant form of PAI-1 less two histidine residues N-terminal in position 2 and 3 exhibit a similar rise in the dynamics of the Cu (II) binding compared to an active wild type PAI-1, suggesting that the structural effect observed is not the result of coordination of Cu ( II) to the histidine residues.

Plasminogen Activator Inhibitor-2 Mouse Recombinant

rAP-1489 Inquiry Ask for price

Recombinant Mouse Plasminogen activator inhibitor 1

MBS963855-002mgEColi 0.02mg(E-Coli)
EUR 320

Recombinant Mouse Plasminogen activator inhibitor 1

MBS963855-002mgYeast 0.02mg(Yeast)
EUR 320

Recombinant Mouse Plasminogen activator inhibitor 1

MBS963855-01mgEColi 0.1mg(E-Coli)
EUR 520

Recombinant Mouse Plasminogen activator inhibitor 1

MBS963855-01mgYeast 0.1mg(Yeast)
EUR 515

Recombinant Mouse Plasminogen activator inhibitor 1

MBS963855-05mgYeast 0.5mg(Yeast)
EUR 1260

Recombinant mouse Plasminogen activator inhibitor 1

MBS9420661-002mg 0.02mg
EUR 380

Recombinant mouse Plasminogen activator inhibitor 1

MBS9420661-01mg 0.1mg
EUR 650

Recombinant mouse Plasminogen activator inhibitor 1

MBS9420661-1mg 1mg
EUR 2525

Recombinant mouse Plasminogen activator inhibitor 1

MBS9420661-5x1mg 5x1mg
EUR 11205

Recombinant Mouse Plasminogen activator inhibitor 1 (Serpine1)

CSB-EP021081MO 2166 mg Ask for price

Recombinant Mouse Plasminogen activator inhibitor 1 (Serpine1)

CSB-EP021081MO-20ug 20ug Ask for price
Description: 23-402aa

Recombinant Mouse Plasminogen activator inhibitor 1(Serpine1)

AP70764 1mg
EUR 2826

Recombinant Mouse Plasminogen activator inhibitor 1(Serpine1)

AP72777 each Ask for price

Recombinant Mouse Plasminogen activator inhibitor 1 (Serpine1)

CSB-YP021081MO 5989 mg Ask for price

Recombinant Mouse Plasminogen activator inhibitor 1 (Serpine1)

CSB-YP021081MO-20ug 20ug Ask for price
Description: 23-402aa

Recombinant Mouse Plasminogen activator inhibitor 1 (Serpine1)

RPC24943-100ug 100ug
EUR 702.9

Recombinant Mouse Plasminogen activator inhibitor 1 (Serpine1)

RPC24943-20ug 20ug
EUR 353.4

Recombinant Mouse Plasminogen activator inhibitor 1 (Serpine1)

RPC21989-100ug 100ug
EUR 705.1

Recombinant Mouse Plasminogen activator inhibitor 1 (Serpine1)

RPC21989-1mg 1mg
EUR 3237

Recombinant Mouse Plasminogen activator inhibitor 1 (Serpine1)

RPC21989-20ug 20ug
EUR 353.4

Recombinant Mouse Plasminogen activator inhibitor 2, macrophage (Serpinb2)

MBS962179-002mgBaculovirus 0.02mg(Baculovirus)
EUR 1285

Recombinant Mouse Plasminogen activator inhibitor 2, macrophage (Serpinb2)

MBS962179-002mgEColi 0.02mg(E-Coli)
EUR 965

Recombinant Mouse Plasminogen activator inhibitor 2, macrophage (Serpinb2)

MBS962179-002mgYeast 0.02mg(Yeast)
EUR 1080

Recombinant Mouse Plasminogen activator inhibitor 2, macrophage (Serpinb2)

MBS962179-01mgEColi 0.1mg(E-Coli)
EUR 1125

Recombinant Mouse Plasminogen activator inhibitor 2, macrophage (Serpinb2)

MBS962179-01mgYeast 0.1mg(Yeast)
EUR 1230

Recombinant Human Plasminogen Activator Inhibitor-2

AP60417 100ug
EUR 1554

Recombinant Human Plasminogen Activator Inhibitor-2

P1567-.01 10ug
EUR 272.8
Description: Peptides & Proteins|Recombinant Proteins

Recombinant Human Plasminogen Activator Inhibitor-2

P1567-.1 100ug
EUR 1560.8
Description: Peptides & Proteins|Recombinant Proteins

Recombinant Human Plasminogen Activator Inhibitor-2

P1567-.5 500ug
EUR 3503.2
Description: Peptides & Proteins|Recombinant Proteins

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

MBS2018222-001mg 0.01mg
EUR 170

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

MBS2018222-005mg 0.05mg
EUR 295

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

MBS2018222-01mg 0.1mg
EUR 450

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

MBS2018222-02mg 0.2mg
EUR 545

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

MBS2018222-05mg 0.5mg
EUR 1040

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

MBS2018365-001mg 0.01mg
EUR 180

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

MBS2018365-005mg 0.05mg
EUR 330

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

MBS2018365-01mg 0.1mg
EUR 500

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

MBS2018365-02mg 0.2mg
EUR 615

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

MBS2018365-05mg 0.5mg
EUR 1170

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

MBS2018456-001mg 0.01mg
EUR 175

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

MBS2018456-005mg 0.05mg
EUR 315

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

MBS2018456-01mg 0.1mg
EUR 475

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

MBS2018456-02mg 0.2mg
EUR 580

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

MBS2018456-05mg 0.5mg
EUR 1100

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

RPA531Hu01 10ug
EUR 170

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

4-RPA531Hu01
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Description: Recombinant Human Plasminogen Activator Inhibitor 2 expressed in: E.coli

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

RPA531Mu01 10ug
EUR 182

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

4-RPA531Mu01
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Description: Recombinant Mouse Plasminogen Activator Inhibitor 2 expressed in: E.coli

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

RPA531Ra01 10ug
EUR 194

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

4-RPA531Ra01
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Description: Recombinant Rat Plasminogen Activator Inhibitor 2 expressed in: E.coli

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

RPU56751-100ug 100ug
EUR 470.4

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

RPU56751-1mg 1mg
EUR 2184

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

RPU56751-50ug 50ug
EUR 385

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

RPU43313-100ug 100ug
EUR 524.7

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

RPU43313-1mg 1mg
EUR 2325.7

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

RPU43313-50ug 50ug
EUR 421.3

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

RPU43314-100ug 100ug
EUR 562.1

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

RPU43314-1mg 1mg
EUR 2489.5

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

RPU43314-50ug 50ug
EUR 451

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

RPU43315-100ug 100ug
EUR 599.5

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

RPU43315-1mg 1mg
EUR 2653.3

Recombinant Plasminogen Activator Inhibitor 2 (PAI2)

RPU43315-50ug 50ug
EUR 480.7

Recombinant human Plasminogen activator inhibitor 2

P1738 100ug Ask for price
Description: Recombinant protein for human Plasminogen activator inhibitor 2

Plasminogen Activator Inhibitor-1 (Recombinant)

20-abx073514
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Plasminogen Activator Inhibitor Type 1, Recombinant, Mouse (PAI-1)

MBS636215-05mg 0.5mg
EUR 1895

Plasminogen Activator Inhibitor Type 1, Recombinant, Mouse (PAI-1)

MBS636215-5x05mg 5x0.5mg
EUR 8310

Recombinant Rat Plasminogen activator inhibitor 1

MBS1189391-002mgEColi 0.02mg(E-Coli)
EUR 320

Recombinant Rat Plasminogen activator inhibitor 1

MBS1189391-01mgEColi 0.1mg(E-Coli)
EUR 520

Recombinant Rat Plasminogen activator inhibitor 1

MBS1189391-1mgEColi 1mg(E-Coli)
EUR 1925

Recombinant Rat Plasminogen activator inhibitor 1

MBS1189391-5x1mgEColi 5x1mg(E-Coli)
EUR 8405

Recombinant Rat Plasminogen activator inhibitor 1

MBS9420662-002mg 0.02mg
EUR 380

Recombinant Rat Plasminogen activator inhibitor 1

MBS9420662-01mg 0.1mg
EUR 650

Recombinant Rat Plasminogen activator inhibitor 1

MBS9420662-1mg 1mg
EUR 2525

Recombinant Rat Plasminogen activator inhibitor 1

MBS9420662-5x1mg 5x1mg
EUR 11205

Recombinant Human Plasminogen Activator Inhibitor-1

MBS143203-0005mg 0.005mg
EUR 240

Recombinant Human Plasminogen Activator Inhibitor-1

MBS143203-0025mg 0.025mg
EUR 310

Recombinant Human Plasminogen Activator Inhibitor-1

MBS143203-1mg 1mg
EUR 3165

Recombinant Human Plasminogen Activator Inhibitor-1

MBS143203-5x1mg 5x1mg
EUR 13925

Plasminogen Activator Inhibitor-1 Human Recombinant

rAP-4753 Inquiry Ask for price

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2105272-001mg 0.01mg
EUR 160

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2105272-005mg 0.05mg
EUR 280

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2105272-01mg 0.1mg
EUR 405

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2105272-02mg 0.2mg
EUR 490

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2105272-05mg 0.5mg
EUR 930

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2030669-001mg 0.01mg
EUR 165

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2030669-005mg 0.05mg
EUR 285

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2030669-01mg 0.1mg
EUR 425

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2030669-02mg 0.2mg
EUR 515

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2030669-05mg 0.5mg
EUR 980

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2010253-001mg 0.01mg
EUR 160

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2010253-005mg 0.05mg
EUR 280

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2010253-01mg 0.1mg
EUR 405

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2010253-02mg 0.2mg
EUR 490

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2010253-05mg 0.5mg
EUR 930

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2029177-001mg 0.01mg
EUR 170

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2029177-005mg 0.05mg
EUR 305

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2029177-01mg 0.1mg
EUR 460

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2029177-02mg 0.2mg
EUR 560

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

MBS2029177-05mg 0.5mg
EUR 1065

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPA532Hu01 10ug
EUR 152

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

4-RPA532Hu01
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Description: Recombinant Human Plasminogen Activator Inhibitor 1 expressed in: E.coli

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPA532Hu02 10ug
EUR 152

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

4-RPA532Hu02
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  • 1 mg
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Description: Recombinant Human Plasminogen Activator Inhibitor 1 expressed in: E.coli

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPA532Mu01 10ug
EUR 160

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

4-RPA532Mu01
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Description: Recombinant Mouse Plasminogen Activator Inhibitor 1 expressed in: E.coli

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPA532Ra01 10ug
EUR 176

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

4-RPA532Ra01
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Description: Recombinant Rat Plasminogen Activator Inhibitor 1 expressed in: E.coli

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPA532Si01 10ug
EUR 164

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPU55545-100ug 100ug
EUR 601.7

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPU55545-1mg 1mg
EUR 2371.2

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPU55545-50ug 50ug
EUR 364.8

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPU56752-100ug 100ug
EUR 470.4

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPU56752-1mg 1mg
EUR 2184

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPU56752-50ug 50ug
EUR 385

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPU43312-100ug 100ug
EUR 468.6

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPU43312-1mg 1mg
EUR 2074.8

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPU43312-50ug 50ug
EUR 376.2

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPU51492-100ug 100ug
EUR 492.8

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPU51492-1mg 1mg
EUR 2184

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPU51492-50ug 50ug
EUR 396

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPU52990-100ug 100ug
EUR 542.3

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPU52990-1mg 1mg
EUR 2402.4

Recombinant Plasminogen Activator Inhibitor 1 (PAI1)

RPU52990-50ug 50ug
EUR 435.6

Recombinant Human Plasminogen activator inhibitor 2 (SERPINB2)

CSB-MP021070HU 4968 mg Ask for price

Recombinant Human Plasminogen activator inhibitor 2 (SERPINB2)

CSB-MP021070HU-20ug 20ug Ask for price
Description: 1-415aa

Recombinant Human Plasminogen activator inhibitor 2 (SERPINB2)

CSB-YP021070HU 5987 mg Ask for price

Recombinant Human Plasminogen activator inhibitor 2 (SERPINB2)

CSB-YP021070HU-20ug 20ug Ask for price
Description: 1-415aa

Recombinant Human Plasminogen activator inhibitor 2 (SERPINB2)

MBS965342-002mgMammalianCell 0.02mg(Mammalian-Cell)
EUR 425

Recombinant Human Plasminogen activator inhibitor 2 (SERPINB2)

MBS965342-002mgYeast 0.02mg(Yeast)
EUR 320

Recombinant Human Plasminogen activator inhibitor 2 (SERPINB2)

MBS965342-01mgMammalianCell 0.1mg(Mammalian-Cell)
EUR 1015

Recombinant Human Plasminogen activator inhibitor 2 (SERPINB2)

MBS965342-01mgYeast 0.1mg(Yeast)
EUR 515

Recombinant Human Plasminogen activator inhibitor 2 (SERPINB2)

MBS965342-05mgYeast 0.5mg(Yeast)
EUR 1260

Recombinant Human Plasminogen activator inhibitor 2 (SERPINB2)

RPC26411-100ug 100ug
EUR 1218.8

Recombinant Human Plasminogen activator inhibitor 2 (SERPINB2)

RPC26411-20ug 20ug
EUR 484

Recombinant Rat Plasminogen activator inhibitor 2 type A

MBS951741-002mgEColi 0.02mg(E-Coli)
EUR 320

Recombinant Rat Plasminogen activator inhibitor 2 type A

MBS951741-002mgYeast 0.02mg(Yeast)
EUR 320

Recombinant Rat Plasminogen activator inhibitor 2 type A

MBS951741-01mgEColi 0.1mg(E-Coli)
EUR 520

Recombinant Rat Plasminogen activator inhibitor 2 type A

MBS951741-01mgYeast 0.1mg(Yeast)
EUR 515

Recombinant Rat Plasminogen activator inhibitor 2 type A

MBS951741-05mgYeast 0.5mg(Yeast)
EUR 1260

Recombinant Rat Plasminogen activator inhibitor 2 type A

MBS9420660-002mg 0.02mg
EUR 380

Recombinant Rat Plasminogen activator inhibitor 2 type A

MBS9420660-01mg 0.1mg
EUR 650

Recombinant Rat Plasminogen activator inhibitor 2 type A

MBS9420660-1mg 1mg
EUR 2525

Recombinant Rat Plasminogen activator inhibitor 2 type A

MBS9420660-5x1mg 5x1mg
EUR 11205

Recombinant Rat Plasminogen activator inhibitor 2 type A

MBS9422489-002mg 0.02mg
EUR 380

Recombinant Rat Plasminogen activator inhibitor 2 type A

MBS9422489-01mg 0.1mg
EUR 650

Recombinant Rat Plasminogen activator inhibitor 2 type A

MBS9422489-05mg 0.5mg
EUR 1655

Recombinant Rat Plasminogen activator inhibitor 2 type A

MBS9422489-5x05mg 5x0.5mg
EUR 7290

Recombinant Human Plasminogen activator inhibitor 1

MBS1265498-002mgEColi 0.02mg(E-Coli)
EUR 255

Recombinant Human Plasminogen activator inhibitor 1

MBS1265498-01mgEColi 0.1mg(E-Coli)
EUR 405

Recombinant Human Plasminogen activator inhibitor 1

MBS1265498-1mgEColi 1mg(E-Coli)
EUR 1425

Recombinant Human Plasminogen activator inhibitor 1

MBS1265498-5x1mgEColi 5x1mg(E-Coli)
EUR 6215

Recombinant human Plasminogen activator inhibitor 1

MBS961954-005mg 0.05mg
EUR 260

Finally, the addition of Cu (II) produces an acceleration of the kinetics of local unfolding of PAI-1 are thought to be on the path to conversion latency. The influence of the ligand on the dynamics of PAI-1 adds another interesting dimension to the mechanism of regulation of PAI-1 stability and function.